Author(s)

Cunbo Wu ¹

Affiliation(s)

¹ Chongqing Mental Health Center, Gele Mountain, Shapingba District, Chongqing, China

Corresponding Author

Cunbo Wu

ABSTRACT

Objective: To clarify the diagnosis of stiff-person syndrome (SPS), distinguish adult-onset Still's diseases (AOSD), and give reasonable treatment. Methods: Laboratory tests of serum and cerebrospinal fluid, rigorous neurological examination and electromyography were performed, while Clonazepam, hormone, gamma globulin, nutritional nerve and symptomatic support treatment were given to the disease. Results: Symptoms of the disease were completely resolved, including no return of fever or rash, no obvious abnormalities on neurological examination, and normal laboratory tests and electromyography. Conclusion: The symptoms of SPS with hyperpyrexia and rash overlap with AOSD, which is easily to be misdiagnosed. Timely and systematic treatment of the disease has a good prognosis, but the risk of recurrence is also high. Clinicians should strengthen the understanding of the disease and carefully choose a reasonable treatment plan.

KEYWORDS

Stiff-person syndronme, adult-onset Still's diseases, rash, hyperpyrexia

CITE THIS PAPER

Cunbo Wu, A Rare Case Report of Stiff-Person Syndrome Analogous to Adult-Onset Still's Disease. MEDS Clinical Medicine (2022) Vol. 3: 95-99. DOI: http://dx.doi.org/10.23977/medsc.2022.030415.

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